3-Hydroxy-2-methylpentanoic acid

CAS: 28892-73-1

Ref. 3D-DBA89273

Produktinformation

• Name: 3-Hydroxy-2-methylpentanoic acid
• Marke: Biosynth
• Beschreibung: 2-Hydroxy-3-methylpentanoic acid (HMVA) is an organic acid generated by L-isoleucine metabolism. There are 4 stereoisomers of HMVA (2S,3S-HMVA, 2R,3R-HMVA, 2S,3R-HMVA and 2R,3S-HMVA). HMVA is found in the urine and blood of normal individuals but in very elevated levels in patients with maple syrup urine disease (MSUD). Maple syrup urine disease (MSUD) is an inherited metabolic disease predominantly characterized by neurological dysfunction including psychomotor/delay/mental retardation.

Chemische Eigenschaften

• Molekulargewicht: 132.16 g/mol
• Formel: C₆H₁₂O₃
• Reinheit: Min. 95%
• Farbe/Form: Clear Liquid