6-Hexadecanoylamino-4-methylumbelliferyl b-D-galactopyranoside - Moscerdam™ biochemical purity

CAS: 94452-17-2

Ref. 3D-EH05989

Produktinformation

• Name: 6-Hexadecanoylamino-4-methylumbelliferyl b-D-galactopyranoside - Moscerdam™ biochemical purity
• Synonyme: 6-HMU galactosideKRB

Beschreibung

Hexadecanoylamino-4-methylumbelliferyl b-D-galactopyranoside is a substrate used for the diagnosis of Krabbe disease. Krabbe disease (globoid cell leukodystrophy/ galactosylceramide lipidosis), is a rare and often fatal lysosomal storage disease that results in progressive damage to the nervous system. It is inherited in an autosomal recessive pattern and involves dysfunctional metabolism of sphingolipids (MG44866 b-D-Galactosylsphingosine - Synthetic)

• Marke: Biosynth

Chemische Eigenschaften

• Molekulargewicht: 591.73 g/mol
• Formel: C₃₂H₄₉NO₉
• Reinheit: Min. 95 Area-%
• Farbe/Form: White Powder