Porphobilinogen

Ref. 3D-FP29489

Produktinformation

• Name: Porphobilinogen
• Synonyme: 5-(Aminomethyl)-4-(carboxymethyl)-1H-pyrrole-3-propanoic acid
• Marke: Biosynth
• Beschreibung: Porphobilinogen is a chemical substance that is created from the breakdown of heme, an iron-containing molecule found in hemoglobin. The enzyme responsible for this process is called porphobilinogen deaminase. Porphobilinogen is also a metabolic intermediate in the synthesis of heme and other substances, such as tetrapyrroles and bilirubin. Porphobilinogen can be used to diagnose various types of infectious diseases, metabolic disorders, and biochemical properties. In order to do so, the patient's blood must be tested for high levels of porphobilinogen. This test can also be used to diagnose erythropoietic protoporphyria (EPP), an inherited metabolic disorder characterized by hypersensitivity to light and skin lesions.

Chemische Eigenschaften

• Molekulargewicht: 226.23 g/mol
• Formel: C₁₀H₁₄N₂O₄
• Reinheit: Min. 95%
• InChl: InChI=1S/C10H14N2O4/c11-4-8-7(3-10(15)16)6(5-12-8)1-2-9(13)14/h5,12H,1-4,11H2,(H,13,14)(H,15,16)
• InChI Key: InChIKey=QSHWIQZFGQKFMA-UHFFFAOYSA-N
• SMILES: NCc1[nH]cc(CCC(=O)O)c1CC(=O)O