Ibiglustat

CAS: 1401090-53-6

Ref. TM-T4473

Produktinformation

• Name: Ibiglustat
• Synonyme: Venglustat, SAR402671, GZ402671
• CAS: 1401090-53-6

Beschreibung

Ibiglustat (GZ402671) is a potent and selective Glucosylceramide synthase inhibitor and ceramide glucosyltransferase inhibitor. Ibiglustat blocks the formation of glucosylceramide (GL-1), a key intermediate in the synthesis of GL-3. Ibiglustat is potentially useful for treating Fabry disease. Fabry disease is a rare lysosomal storage disorder, which results in abnormal tissue deposits of a particular fatty substance called globotriaosylceramide (GL-3 or Gb3) throughout the body.

• Marke: Targetmol

Chemische Eigenschaften

• Molekulargewicht: 389.49
• Formel: C₂₀H₂₄FN₃O₂S
• Reinheit: 99.14%
• Farbe/Form: Solid