N-Iso Valerylglycine-13C2,15N

CAS: 16284-60-9

Ref. TR-I917603

Produktinformation

• Name: N-Iso Valerylglycine-13C2,15N
• Synonyme: N-(3-Methyl-1-oxobutyl)glycine-13C2,15N, N-Isovalerylglycine-13C2,15N, Isovalerylglycine-13C2,15N, N-Isovaleroylglycine-13C2,15N, 2-(3-Methylbutanamido)acetic acid, 2-(3-Methylbutanoylamino)acetic acid, Glycine, N-(3-methyl-1-oxobutyl)-, Glycine, N-isovaleryl-, Isovalerylglycine, N-(3-Methyl-1-oxobutyl)glycine, N-(3-methylbutanoyl)glycine, N-Isovaleroylglycine, N-Isovalerylglycine

Beschreibung

Applications N-Iso Valerylglycine-13C2,15N is a labelled analogue of N-Iso Valerylglycine (I917600(P)), which is diagnostic tool for many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism.
References Tanaka, K., et al.: J. Biol. Chem., 242, 2966 (1967); Bonafe, L., et al.: Mol. Gen. Metab., 69, 311 (2000);

• Marke: TRC

Chemische Eigenschaften

• Molekulargewicht: 162.162
• Formel: C₂C₅H₁₃NO₃
• Farbe/Form: White To Off-White
• InChl: InChI=1S/C7H13NO3/c1-5(2)3-6(9)8-4-7(10)11/h5H,3-4H2,1-2H3,(H,8,9)(H,10,11)/i4+1,7+1,8+1
• InChI Key: InChIKey=ZRQXMKMBBMNNQC-DPZTXFNWSA-N
• SMILES: CC(C)CC(=O)[15NH][13CH2][13C](=O)O