3-Methylglutaconic Acid

CAS: 5746-90-7

Ref. TR-M311565

Produktinformation

• Name: 3-Methylglutaconic Acid
• Synonyme: 3-Methyl-2-pentenedioic Acid, 3-Methyl-glutaconic Acid, NSC 249232, β-Methylglutaconic Acid, (2E)-3-Methyl-2-pentenedioic acid, 2-Pentenedioic acid, 3-methyl-, 2-pentenedioic acid, 3-methyl-, (2E)-, 3-Methyl-2-pentenedioic acid, 3-Methylglutaconic acid, Glutaconic acid, 3-methyl-, β-Methylglutaconic acid, (2E)-3-Methylpent-2-enedioic acid

Beschreibung

Stability Hygroscopic
Applications 3-Methylglutaconic acid is a glutarate which builds up in the urine in 3-methylglutaconic aciduria. 3-methylglutaconic aciduria is a term used to describe five different disorders that impair the functioning of energy-producing centers within cells (mitochondria)
References Walsh, R., et al.: J. Inherit. Metab. Dis., 22, 251 (1999); Gonzalez, I., et al.: Am J Med Genet A., 134, 409 (2005); MacKenzie, J., et al.: Biochim Biophys Acta., 1772, 509 (2007)

• Marke: TRC

Chemische Eigenschaften

• Molekulargewicht: 144.13
• Formel: C₆H₈O₄
• Farbe/Form: Neat
• InChl: InChI=1S/C6H8O4/c1-4(2-5(7)8)3-6(9)10/h2H,3H2,1H3,(H,7,8)(H,9,10)/b4-2+
• InChI Key: InChIKey=WKRBKYFIJPGYQC-DUXPYHPUSA-N
• SMILES: C/C(=C\C(=O)O)CC(=O)O