Globotriaosylceramide Sphingosine-d2,13C tert-Butyldimethylsilyl
CAS : 126550-86-5
Ref. TR-G410642
25mg | Arrêté |
Informations sur le produit
- (2S,3R,4E)-2-Amino-3-((tert-butyldimethylsilyl)oxy)-4-octadecenyl-d2,13C O-α-D-Galactopyranosyl-(1→4)-O-β-D-galactopyranosyl-(1→4)-β-D-glucopyranoside
- lyso-Gb3-d2,13C tert-Butyldimethylsilyl
- (2R,3R,4S,5R,6R)-2-(((2R,3R,4R,5R,6S)-6-(((2R,3S,4R,5R,6R)-6-(((2S,3R,E)-2-Amino-3-((tert-butyldimethylsilyl)oxy)octadec-4-en-1-yl-d2, 13C)oxy)-4,5-dihydroxy-2-(hydroxymethyl)tetrahydro-2H-pyran-3-yl)oxy)-4,5-dihydroxy-2-(hydroxymethyl)tetrahydro-2H-pyran-3-yl)oxy)-6-(hydroxymethyl)tetrahydro-2H-pyran-3,4,5-triol
- Globotriaosylsphingosine
- Α-D-Gal-(1→4)-Β-D-Gal-(1→4)-Β-D-Glc-1→O-Sphingosine
- Globotriaosyl Lysosphingolipid
- Globotriaosylsphingosine from porcine blood
- (2S,3R,4E)-2-amino-3-hydroxyoctadec-4-en-1-yl alpha-D-galactopyranosyl-(1->4)-beta-D-galactopyranosyl-(1->4)-beta-D-glucopyranoside
Applications Globotriaosylceramide Sphingosine-d2,13C tert-Butyldimethylsilyl is a labeled Fabry disease biomarker.
References Dupont, F.O., et. al.: Curr. Med. Chem., 20, 280 (2013); Liao, H., et. al.: Clinica Chimica Acta, 426, 114 (2013)