2-Pivalamidoacetic acid
CAS: 23891-96-5
Rif. 3D-FP154890
25mg | 136,00 € | ||
50mg | 195,00 € | ||
100mg | 325,00 € | ||
250mg | 454,00 € | ||
500mg | 734,00 € |
Informazioni sul prodotto
2-Pivalamidoacetic acid is an acylglycine. It is a competitive inhibitor of the enzyme carnitine acetyltransferase and lowers levels of carnitine in plasma and muscle tissue. This drug has been used to treat acidemia in humans caused by multiple-reaction monitoring deficiency, which can lead to lactic acidosis, muscle weakness, and severe neurologic problems. 2-Pivalamidoacetic acid has also been used as an oral treatment for long-term treatment of neonatal acylglycinemia type 1 (AG1) due to dehydrogenase deficiency, which can cause growth failure, hypotonia, and respiratory distress.
Proprietà chimiche
Richiesta tecnica su: 3D-FP154890 2-Pivalamidoacetic acid
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