PHS Protein, Human, Recombinant (His)
Ref. TM-TMPJ-01043
| 1mg | 2,602.00 € | ||
| 10µg | 185.00 € | ||
| 50µg | 537.00 € | ||
| 500µg | 1,811.00 € |
Product Information
- 4-Alpha-Hydroxy-Tetrahydropterin Dehydratase, Pterin-4-α-Carbinolamine Dehydratase, Phenylalanine Hydroxylase-Stimulating Protein, Dimerization Cofactor of Hepatocyte Nuclear Factor 1-Alpha, PHS, Dimerization Cofactor of HNF1, Dimerization Cofactor of Hepatocyte Nuclear Factor 1-α, 4-α-Hydroxy-Tetrahydropterin Dehydratase, DCoH, Pterin Carbinolami, Pterin-4-Alpha-Carbinolamine Dehydratase
Pterin-4-α-Carbinolamine Dehydratase (PCBD1) is the founding member of the Pterin-4-α-Carbinolamine Dehydratase Family. PCBD1 is involved in Tetrahydrobiopterin biosynthesis. It seems to prevent the formation of 7-Pterins and accelerate the formation of Quinonoid-BH2. Furthermore, PCBD1 regulates the homodimerization of the transcription factor Hepatocyte Nuclear Factor 1 (HNF1) and enhances its transcriptional activity. Defects in PCBD1 are the cause of BH4-Deficient Hyperphenylalaninemia Type D (HPABH4D). HPABH4D is characterized by the excretion of 7-substituted Pterins in the urine of affected patients.
Chemical properties
Technical inquiry about: TM-TMPJ-01043 PHS Protein, Human, Recombinant (His)
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