N-Isobutyryl-d7-glycine

CAS: 1330037-23-4

Ref. TR-I780753

Product Information

• Name: N-Isobutyryl-d7-glycine
• Synonyms: N-(2-methyl-1-oxopropyl-d7)glycine

Description

Applications N-Isobutyryl-d7-glycine is labelled N-Isobutyrylglycine (I780750) which is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isobutyrylglycine detection is also used in the diagnosis of isobutyryl-CoA dehydrogenase deficiency.
References Costa, C. G. et al.: J. Pharmac. Biomed. Anal., 21, 1215 (2000); Bonafe, L. et al.: Mol. Gen. Metab., 69, 311 (2000); Sass, J. et al.: J. Inher. Metab. Dis., 27, 741 (2004);

• Brand: TRC

Chemical properties

• Molecular weight: 152.2
• Formula: C₆H₄D₇NO₃
• Color/Form: White To Off-White
• InChI: InChI=1S/C6H11NO3/c1-4(2)6(10)7-3-5(8)9/h4H,3H2,1-2H3,(H,7,10)(H,8,9)/i1D3,2D3,4D
• InChI key: InChIKey=DCICDMMXFIELDF-UAVYNJCWSA-N
• SMILES: [2H]C([2H])([2H])C([2H])(C(=O)NCC(=O)O)C([2H])([2H])[2H]