Ibiglustat

CAS: 1401090-53-6

Ref. TM-T4473

Informação sobre produto

• Nome: Ibiglustat
• Sinónimos: Venglustat, SAR402671, GZ402671
• CAS: 1401090-53-6

Descrição

Ibiglustat (GZ402671) is a potent and selective Glucosylceramide synthase inhibitor and ceramide glucosyltransferase inhibitor. Ibiglustat blocks the formation of glucosylceramide (GL-1), a key intermediate in the synthesis of GL-3. Ibiglustat is potentially useful for treating Fabry disease. Fabry disease is a rare lysosomal storage disorder, which results in abnormal tissue deposits of a particular fatty substance called globotriaosylceramide (GL-3 or Gb3) throughout the body.

• Marca: Targetmol

Propriedades químicas

• Peso molecular: 389.49
• Fórmula: C₂₀H₂₄FN₃O₂S
• Pureza: 99.14%
• Cor/forma: Solid