CAS 256928-75-3

2-Methylbutyrylcarnitine

Description:

2-Methylbutyrylcarnitine is a derivative of carnitine, a quaternary ammonium compound involved in the transport of fatty acids into the mitochondria for energy production. This compound is characterized by its structure, which includes a methyl group at the second position of the butyric acid chain, contributing to its unique properties. It is typically found in biological systems and is associated with metabolic processes, particularly in the context of fatty acid metabolism. The presence of the carnitine moiety allows it to play a role in cellular energy metabolism and may be involved in various biochemical pathways. 2-Methylbutyrylcarnitine is often studied in relation to its potential implications in metabolic disorders and its role as a biomarker. Its solubility in water and organic solvents can vary, influencing its behavior in biological systems. As with many carnitine derivatives, it may exhibit specific interactions with enzymes and transport proteins, impacting its physiological functions. Overall, 2-Methylbutyrylcarnitine is an important compound in the study of metabolism and energy production in living organisms.

Formula: C₁₂H₂₃NO₄

InChI: InChI=1S/C12H23NO4/c1-6-9(2)12(16)17-10(7-11(14)15)8-13(3,4)5/h9-10H,6-8H2,1-5H3/t9?,10-/m1/s1

InChI key: InChIKey=IHCPDBBYTYJYIL-QVDQXJPCSA-N

SMILES: [C@H](OC(C(CC)C)=O)(C[N+](C)(C)C)CC([O-])=O

Synonyms:

• 2-Methylbutyrylcarnitine
• 1-Propanaminium, 3-carboxy-N,N,N-trimethyl-2-(2-methyl-1-oxobutoxy)-, inner salt, (2R)-

(3R)-3-((2-Methylbutanoyl)oxy)-4-(trimethylammonio)butanoate

CAS: 256928-75-3

Formula: C₁₂H₂₃NO₄

Purity: 95%

Molecular weight: 245.3153

Ref: IN-DA0031XM

2-Methylbutyrylcarnitine

CAS: 256928-75-3

2-Methylbutyrylcarnitine

Purity: 98%

Ref: 54-OR1037176

2-Methylbutyrylcarnitine

CAS: 256928-75-3

2-Methylbutyrylcarnitine, a fatty acid metabolite from pyruvate pathway, indicates metabolic diseases, found in blood and urine.

Formula: C₁₂H₂₃NO₄

Color and Shape: Solid

Molecular weight: 245.32

Ref: TM-T73748

2-Methylbutyryl-L-Carnitine Chloride(Mixture of Diastereomers)

Controlled Product

CAS: 256928-75-3

Applications The methylated analogue of Isobutyryl L-Carnitine (I780500). 2-Methylbutyryl-L-Carnitine is one of the acylcarnitines profiled from blood or plasma samples in the diagnosis of inborn errors of metabolism.
References Rashed, M.S. et al.: Pediat. Res., 38, 324 (1995); Frazier, D.M. et al.: J. Inher. Metab. Dis., 29, 76 (2006);

Formula: C₁₂H₂₄NO₄·Cl

Color and Shape: Neat

Molecular weight: 281.78

Ref: TR-M294375

2-Methylbutyryl-L-Carnitine-d3 Chloride

Controlled Product

CAS: 256928-75-3

Applications The labelled methylated analogue of Isobutyryl L-Carnitine (I780500). 2-Methylbutyryl-L-Carnitine is one of the acylcarnitines profiled from blood or plasma samples in the diagnosis of inborn errors of metabolism.
References Rashed, M.S. et al.: Pediat. Res., 38, 324 (1995); Frazier, D.M. et al.: J. Inher. Metab. Dis., 29, 76 (2006);

Formula: C₁₂D₃H₂₁NO₄·Cl

Color and Shape: Neat

Molecular weight: 284.79

Ref: TR-M294377