CAS 31023-24-2

Isovalerylcarnitine

Description:

Isovalerylcarnitine is a derivative of carnitine, which plays a crucial role in the transport of fatty acids into the mitochondria for energy production. It is characterized by its branched-chain structure, which includes an isovaleryl group attached to the carnitine backbone. This compound is typically found in biological systems and is involved in metabolic processes, particularly in the metabolism of branched-chain amino acids. Isovalerylcarnitine is often studied in the context of metabolic disorders, as its levels can indicate specific enzymatic deficiencies or disruptions in fatty acid metabolism. The substance is soluble in water and exhibits a polar nature due to the presence of hydroxyl and quaternary ammonium functional groups. Its biological significance is underscored by its potential role as a biomarker in certain metabolic conditions. Additionally, research into isovalerylcarnitine may provide insights into therapeutic applications, particularly in conditions related to energy metabolism and mitochondrial function.

Formula: C₁₂H₂₃NO₄

InChI: InChI=1S/C12H23NO4/c1-9(2)6-12(16)17-10(7-11(14)15)8-13(3,4)5/h9-10H,6-8H2,1-5H3/t10-/m1/s1

InChI key: InChIKey=IGQBPDJNUXPEMT-SNVBAGLBSA-N

SMILES: [C@H](OC(CC(C)C)=O)(C[N+](C)(C)C)CC([O-])=O

Synonyms:

• (3R)-3-(3-Methylbutanoyloxy)-4-(trimethylazaniumyl)butanoate
• (3R)-3-[(3-methylbutanoyl)oxy]-4-(trimethylammonio)butanoate
• (R)-3-((3-Methylbutanoyl)oxy)-4-(trimethylammonio)butanoate
• (R)-3-Carboxy-N,N,N-trimethyl-2-(3-methyl-1-oxobutoxy)-1-propanaminium inner salt
• 1-Propanaminium, 3-carboxy-N,N,N-trimethyl-2-(3-methyl-1-oxobutoxy)-, inner salt, (2R)-
• 1-Propanaminium, 3-carboxy-N,N,N-trimethyl-2-(3-methyl-1-oxobutoxy)-, inner salt, (R)-
• 3-[(3-Methylbutanoyl)Oxy]-4-(Trimethylammonio)Butanoate
• Ammonium, (3-carboxy-2-hydroxypropyl)trimethyl-, hydroxide, inner salt, isovalerate, <span class="text-smallcaps">L</span>-
• Isovaleryl <span class="text-smallcaps">L</span>-carnitine
• Isovalerylcarnitine
• Isovaleryl L-carnitine

1-Propanaminium, 3-carboxy-N,N,N-trimethyl-2-(3-methyl-1-oxobutoxy)-, inner salt, (2R)-

CAS: 31023-24-2

Formula: C₁₂H₂₃NO₄

Purity: 94%

Color and Shape: Solid

Molecular weight: 245.3153

Ref: IN-DA0031XN

(R)-3-((3-Methylbutanoyl)oxy)-4-(trimethylammonio)butanoate

CAS: 31023-24-2

(R)-3-((3-Methylbutanoyl)oxy)-4-(trimethylammonio)butanoate

Purity: 98%

Molecular weight: 245.32g/mol

Ref: 54-OR1067294

3-Methylbutyryl-DL-carnitine-d9 HCl (N,N,N-trimethyl-d9)(N-Isovalerylcarnitine)

CAS: 31023-24-2

Formula: HOOCCH₂CHOCOCH₂CH(CH₃)₂CH₂N(CD₃)₃Cl

Purity: 99 atom % D

Color and Shape: White Solid

Molecular weight: 290.19588

Ref: 3U-D6648

Isovalerylcarnitine

CAS: 31023-24-2

Isovalerylcarnitine (3-methylbutyrylcarnitine) is a selective effective calpain activator that can promote cell apoptosis and is related to isovaleric acidemia.

Formula: C₁₂H₂₃NO₄

Purity: 98.24%

Color and Shape: Solid

Molecular weight: 245.32

Ref: TM-T19384

Isovalerylcarnitine

CAS: 31023-24-2

Isovalerylcarnitine is a diagnostic agent that can be used to measure carnitine levels in biological samples, such as maternal blood. Isovalerylcarnitine has been shown to be elevated in patients with metabolic disorders, including carnitine deficiency, and ethylmalonic aciduria. It is also used to measure the levels of isovalerylcarnitine and trigeminal nerve function in patients with trigeminal neuralgia. Isovalerylcarnitine can be measured using LC-MS/MS methods, which are highly specific and accurate. This test is most often performed on blood serum or plasma samples.

Formula: C₁₂H₂₃NO₄

Purity: Min. 95%

Color and Shape: Powder

Molecular weight: 245.32 g/mol

Ref: 3D-GBA02324