N-Butyldeoxynojirimycin
CAS: 72599-27-0
Ref. 3D-MB06729
1mg | 138.00 € | ||
2mg | 186.00 € | ||
5mg | 364.00 € | ||
10mg | 492.00 € | ||
25mg | 940.00 € |
Product Information
- ZavescaMiglustatOGT 918NB-DNJ
- N-Butyl-1-deoxynojirimycin
- 3,4,5-Piperidinetriol, 1-butyl-2-(hydroxymethyl)-, [2R-(2α,3β,4α,5β)]-
- 3,4,5-Piperidinetriol, 1-butyl-2-(hydroxymethyl)-, (2R,3R,4R,5S)-
- (2R,3R,4R,5S)-1-Butyl-2-(hydroxymethyl)-3,4,5-piperidinetriol
Competitive inhibitor of ceramide-glycosyltransferase used for substrate reduction therapy in lysosomal storage disorders. It inhibits glucosylceramide synthase, which catalyses the initial step in glycosphingolipid biosynthetic pathway. This compound delays the onset of symptoms in type 1 Gaucher disease, Sandhoff disease and Tay-Sachs disease. It also reduces brain abnormalities in mucolipidosis type IV.
Chemical properties
Technical inquiry about: 3D-MB06729 N-Butyldeoxynojirimycin
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